Primitive neuroectodermal tumor of the kidney: a rare case

Abstract Background Primitive neuroectodermal tumor commonly occurs in bones and is equivalent to Ewing’s sarcoma. Very few cases have been reported the literature they had a very different presentation aggressive behavior. Case We present case of young 23-year-old male who presented with complaints pain left lumbar region abdomen since 8 months hematuria off on. CT scan was done which revealed large heterogeneously enhancing mass lesion arising from superior mid-pole kidney showing multiple non-enhancing necrotic areas. A diagnosis renal cell carcinoma kept. Through transperitoneal approach, approached radical nephrectomy done. The histopathology report cells be positive for CD99 focally Vimentin negative cytokeratin thereby making primary (PNET). Conclusions Renal PNET rare malignancy that should kept differential SOL especially when it presenting feature adolescent adult. It has course multimodal therapy considered its treatment